Articulo
Vitamin E Dietary Supplementation Improves Neurological Symptoms and Decreases c-Abl/p73 Activation in Niemann-Pick C Mice
Nutrients
Registro en:
15090007
15090007
Autor
Marín, Tamara
Contreras, Pablo
Castro, Juan Francisco
Chamorro, David
Balboa, Elisa
Bosch-Morató, Mónica
Muñoz, Francisco
Alvarez, Alejandra
Zanlungo, Silvana
Institución
Resumen
Niemann-Pick C (NPC) disease is a fatal neurodegenerative disorder characterized by the accumulation of free cholesterol in lysosomes. We have previously reported that oxidative stress is the main upstream stimulus activating the proapoptotic c-Abl/p73 pa FONDAP FONDAP