dc.creatorVega-Briceño,Luis
dc.creatorContreras E,Ilse
dc.creatorSánchez D,Ignacio
dc.creatorBertrand N,Pablo
dc.date2004-07-01
dc.date.accessioned2017-03-07T15:20:47Z
dc.date.available2017-03-07T15:20:47Z
dc.identifierhttp://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0034-98872004000700012
dc.identifier.urihttp://repositorioslatinoamericanos.uchile.cl/handle/2250/383129
dc.descriptionOsteogenesis imperfecta (OI) is an heterogeneous group of genetic disorders that affect connective tissue integrity. Severe forms cause chest deformities, sometimes associated to alveolar hypoventilation. We report a 4 months old infant with OI type III, who developed respiratory failure (RF) due to a bronchiolitis and required mechanical ventilation. Weaning progressed successfully to a nasal bi-level Positive Airway Pressure (n-BiPAP) device. Clinical follow up showed a normal cognitive development and growth. Respiratory condition, blood gases and ventilation status were in normal ranges. Non invasive ventilation, associated to careful monitoring may avoid tracheostomy and its complications in infants with OI (Rev Méd Chile 2004; 132: 861-4)
dc.formattext/html
dc.languagees
dc.publisherSociedad Médica de Santiago
dc.sourceRevista médica de Chile v.132 n.7 2004
dc.subjectBronchiolitis
dc.subjectOsteogenesis imperfecta
dc.subjectNasal continuous positive airway pressure
dc.titleUso precoz del BiPAP en el tratamiento de la insuficiencia respiratoria en un lactante con osteogénesis imperfecta: Case report
dc.typeArtículos de revistas


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