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Myocardial Alterations in the Murine Model of Fabry Disease Can Be Reversed by Enzyme Replacement Therapy
(Pulsus Group Inc, 2011-05)
Background: Fabry disease results from deficiency of alpha-galactosidase A (AGA), causing lysosomal storage of globotriaosylceramide in heart and other tissues. Since 2003, enzymatic replacement therapy with recombinant ...
Busca de parceiros físicos da proteína CRABP2, utilizando o sistema de duplo-híbrido em Saccharomyces cerevisae
(Universidade Estadual Paulista (UNESP), 2015)
Busca de parceiros físicos da proteína CRABP2, utilizando o sistema de duplo-híbrido em Saccharomyces cerevisae
(Universidade Estadual Paulista (Unesp), 2015)
Dilution-to-stimulation/extinction : a "top-down" strategy to develop a minimal, effective and versatile lignocellulolytic microbial consortium
(Universidad de los AndesMaestría en Ciencias BiológicasFacultad de CienciasDepartamento de Ciencias Biológicas, 2020)
The enzymes secreted by lignocellulolytic microbial consortia could potentially boost saccharification processes in biorefineries. Here, we developed a minimal and effective lignocellulolytic microbial consortium (MELMC) ...
Endo-beta-mannanase from the endosperm of seeds of Sesbania virgata (Cav.) Pers. (Leguminosae): purification, characterisation and its dual role in germination and early seedling growthEndo-beta-mananase do endosperma de sementes de Sesbania virgata (Cav.) Pers. (Leguminosae): purificação, caracterização e seu duplo papel na germinação e crescimento inicial da plântula
(Brazilian Journal of Plant Physiology, 2006)
Estudo da homeostase lisossômica e caracterização de fibroblastos de pacientes com doença de Fabry em cultura celular
(Universidade Federal de São Paulo (UNIFESP), 2017-01-31)
Fabry disease is one of the lysosomal storage diseases which has a X-linked recessive inheritance. A mutation in GLA gene, causes α-galactosidase A (α-Gal A) deficiency, that with the crescent accumulation of globotriaosylceramide ...