Incontinentia pigmenti presenting as hypodontia in a 3-year-old girl: A case report

dc.contributorUniversidade Estadual Paulista (UNESP)
dc.creatorKitakawa, Dárcio
dc.creatorFontes, Patrícia Campos
dc.creatorMagalhães, Fernando Augusto Cintra
dc.creatorAlmeida, Janete Dias
dc.creatorCabral, Luiz Antonio Guimarães
dc.date2014-05-27T11:24:04Z
dc.date2016-10-25T18:27:48Z
dc.date2014-05-27T11:24:04Z
dc.date2016-10-25T18:27:48Z
dc.date2009-12-01
dc.date.accessioned2017-04-06T01:38:33Z
dc.date.available2017-04-06T01:38:33Z
dc.identifierJournal of Medical Case Reports, v. 3.
dc.identifier1752-1947
dc.identifierhttp://hdl.handle.net/11449/71316
dc.identifierhttp://acervodigital.unesp.br/handle/11449/71316
dc.identifier10.1186/1752-1947-3-116
dc.identifier2-s2.0-73849123776.pdf
dc.identifier2-s2.0-73849123776
dc.identifierhttp://dx.doi.org/10.1186/1752-1947-3-116
dc.identifier.urihttp://repositorioslatinoamericanos.uchile.cl/handle/2250/892318
dc.descriptionIntroduction. Incontinentia pigmenti or Bloch-Sulzberger syndrome is a rare X-linked dominant disease that mainly affects the skin, eyes, hair, central nervous system and teeth. The disease is predominant among women. Although dermatologic manifestations are among the most important aspects for the diagnosis of the syndrome, they are less damaging to the patient and do not require treatment. However, oral involvement characterized by hypodontia of deciduous and permanent teeth is important for the diagnosis and treatment of the patient. Case presentation. We report the case of a 3-year-old girl with ophthalmologic and neurologic disturbances, cutaneous manifestations and hypodontia. Since the patient did not present more damaging manifestations such as neurologic and/or ophthalmologic problems, her most severe complications were related to dental anomalies. The importance of integrated dental treatment, which combines pediatric dentistry, orthodontics and conventional prosthesis, is emphasized. Conclusion. Hypodontia is a frequent finding in incontinentia pigmenti, and dentists should be aware of this condition in order to help with the diagnosis. © 2009 Kitakawa et al; licensee BioMed Central Ltd.
dc.languageeng
dc.relationJournal of Medical Case Reports
dc.rightsinfo:eu-repo/semantics/openAccess
dc.subjectaciclovir
dc.subjectanamnesis
dc.subjectblister
dc.subjectcase report
dc.subjectchild
dc.subjectdentistry
dc.subjecteye disease
dc.subjectfemale
dc.subjectherpes zoster
dc.subjecthuman
dc.subjecthypodontia
dc.subjectincontinentia pigmenti
dc.subjectmouth examination
dc.subjectneurologic disease
dc.subjectorthodontics
dc.subjectpanoramic radiography
dc.subjectphysical examination
dc.subjectpreschool child
dc.subjectpriority journal
dc.subjectprosthesis
dc.subjectskin disease
dc.subjectstrabismus
dc.subjecttooth malformation
dc.titleIncontinentia pigmenti presenting as hypodontia in a 3-year-old girl: A case report
dc.typeOtro


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