Malformação de chiari do tipo II sintomática

dc.creatorSalomão, José Francisco Manganelli
dc.creatorBellas, Antônio R.
dc.creatorLeibinger, Renê D.
dc.creatorBarbosa, Ana Paula A.
dc.creatorBrandão, Maria Anna P. B.
dc.date2013-03-05T14:58:45Z
dc.date2013-03-05T14:58:45Z
dc.date1998
dc.date.accessioned2023-09-26T20:42:09Z
dc.date.available2023-09-26T20:42:09Z
dc.identifierSALOMÃO, José Francisco Manganelli et al. Malformação de chiari do tipo II sintomática. Arquivos de Neuro-Psiquiatria, São Paulo, v. 56, n. 1, p. 98-106, 1998.
dc.identifier0004-282X
dc.identifierhttps://www.arca.fiocruz.br/handle/icict/6347
dc.identifier10.1590/S0004-282X1998000100016
dc.identifier.urihttps://repositorioslatinoamericanos.uchile.cl/handle/2250/8862307
dc.descriptionOs autores analisam uma série de 17 crianças portadoras de mielodisplasias que desenvolveram sinais e sintomas da malformação de Chiari do tipo II. De acordo com a idade, dois grupos ficaram bem definidos: Grupo I, crianças no primeiro ano de vida, em que predominaram sinais e sintomas de comprometimento do tronco encefálico e nervos cranianos bulbares (n=13); Grupo II, composto por crianças com idade superior a um ano, em que as principais manifestações foram dor cervical e sinais cerebelares (n=4). O resultado do tratamento cirúrgico nos dois grupos foi distinto: enquanto a mortalidade no Grupo I atingiu 46,1%, nenhum paciente do Grupo II veio a falecer. O tratamento inicial consistiu na instalação ou revisão de derivação ventricular, sendo a descompressão crânio-vertebral reservada àqueles que não se beneficiaram com esses procedimentos. Os autores enfatizam a necessidade do imediato reconhecimento e tratamento do quadro, de modo a se obter resultados satisfatórios.
dc.descriptionThe Chiari type II malformation is the leading cause of death in infants with myelomeningocele. The authors report 17 cases of symptomatic Chiari type II malformation occurring in two distinct age dependent population. In Group I, 13 neonates and infants in the first year of life presented with cranial nerve and brain stem dysfunction characterized by vocal cord paralysis, apnea, dysphagia and laryngeal stridor. In Group II, 4 patients developed signs and symptoms after the first year of life. In this group, the presentation was more insidious and included neck pain and cerebellar manifestations. The surgical treatment consisted initially in shunt implantation or revision and when there was no improvement, posterior fossa decompression was performed. The response to the surgical treatment differed considerably between the two groups: older patients improved promptly after surgery and there was no casualties; in newborn and infants, especially those under 6 months of age, the mortality rate was 46.1%. The authors stress that prompt diagnosis and surgical intervention should be performed in order to produce a favorable outcome.
dc.formatapplication/pdf
dc.languagepor
dc.publisherAcademia Brasileira de Neurologia
dc.relationKoehler PJ. Historical vignette: Chiari´s description of cerebellar ectopy (1891). With a summary of Cleland´s and Arnold´s contributions and some early observations on neural-tube defects. J Neurosurg 1991;75:823-826.
dc.relationCarmel PW. Congenital syringomyelia. In Batzdorf U (ed). Syringomyelia: current concepts in diagnosis and treatment. Baltimore: Williams & Wilkins, 1991:140-150.
dc.relationCameron AH. The Arnold-Chiari and other neuroanatomical malformations associated with spina bifida. J Pathol 1957;73:195-211.
dc.relationGilbert JN, Jones KL, Rorke LB, Chernoff GF, James HE. Central nervous system anomalies with associated meningocele hydrocephalus, and the Arnold-Chiari malformation: reappraisal of theories regarding the pathogenesis of posterior neural tube closure defects. Neurosurgery 1986;18:559-564.
dc.relationPeach B. Arnold Chiari malformation: anatomic features of 20 cases. Arch Neurol 1965;12:613-621.
dc.relationPenfield W, Coburn DF. Arnold-Chiari malformation and its operative treatment. Arch Neurol Psychiat 1938;40:328-336.
dc.relationCharney EB, Rorke LB, Sutton LN, Schut L. Management of Chiari II complications in infants with myelomeningocele. J Pediatr 1987;111:364-371.
dc.relationRauzzino M, Oakes WJ. Chiari II malformation and syringomyelia. Neurosurg Clin N Am 1995;6:293-309.
dc.relationVandertop WP, Asai A, Hoffman HJ, et al. Surgical decompression for symptomatic Chiari II malformation in neonates with myelomeningocele. J Neurosurg 1992;77:541-544.
dc.relationDahl M, Ahlsten G, Carlson H, et al. Neurological dysfunction above cele level in children with spina bifida cystica: a prospective study to three years. Dev Med Child Neurol 1995;37:30-40.
dc.relationHahn YS. Open myelomeningocele. Neurosurg Clin N Am 1995;6:231-241.
dc.relationMcLone DG. Results of treatment of children born with a myelomeningocele. Clin Neurosurg 1983;30:407-435.
dc.relationMcLone DG. Continuing concepts in management of spina bifida. Pediatr Neurosurg 1992;18:254-256.
dc.relationSieben RL, Hamida MB, Shulman K. Multiple cranial nerve deficits associated with the Arnold-Chiari malformation. Neurology 1971;21:673-681.
dc.relationGriebel ML, Oakes WJ, Morley G. The Chiari malformation associated with mielomeningocele. In Rekate HL (ed). Comprehensive management of spina bifida. Boca Raton: CRC Press, 1991:67-92.
dc.relationGardner WJ. Hydrodynamic mechanism of syringomyelia: its relationship to myelocele. J Neurol Neurosurg Psychiatry 1965;28:247-259.
dc.relationGardner WJ. Myelocele: rupture of the neural tube? Clin Neurosurg 1968;15:57-79.
dc.relationGardner WJ. The dysraphic states: from syringomyelia to anencephaly. Amsterdam: Excerpta Medica, 1973.
dc.relationMcLone DG, Knepper PA. The cause of the Chiari malformation: a unified theory. Pediatr Neurosci 1989;15:1-12.
dc.relationMcCullough DC, Johnson DL Myelomeningocele repair: technical considerations and complications. Concepts Pediat Neurosurg 1988;8:29-40.
dc.relationPark TS, Hoffman HJ, Hendrick EB, Humphreys RP. Experience with surgical decompression of the Arnold-Chiari malformation in young infants with myelomeningocele. Neurosurgery 1983;13:147-152.
dc.relationVenes JL. Multiple cranial nerve palsies in an infant with Arnold-Chiari malformation. Dev Med Child Neurol 1974;16:817-820.
dc.relationEpstein F. Meningomyelocele: “pitfalls” in early and late management. Clin Neurosurg 1983;30:366-383.
dc.relationBell WO,. Charney EB, Bruce DA, Schut L. Symptomatic Arnold-Chiari malformation: review of experience with 22 cases. J Neurosurg 1987;66:812-816.
dc.relationWealthall SR, Whittaker GE, Greenwood N. The relationship of apnoea and stridor in spina bifida occulta to the unexplained infant’s deaths. Dev Med Child Neurol 1974;16(Suppl):107-116.
dc.relationPollack IF, Pang D, Kocoshis S, Putnan P. Neurogenic dysphagia resulting from Chiari malformations. Neurosurgery 1992;30:709-719.
dc.relationCochrane DD, Addeley R, White CP, Norman P, Steinbok P. Apnea in patients with myelomeningocele. Pediatr Neurosurg 1991;16:232-239.
dc.relationCarmel PW. Management of Chiari malformations in childhood. Clin Neurosurg 1983;30:385-406.
dc.relationHoffman HJ, Hendrick EB, Humphreys RP. Manifestations and management of Arnold-Chiari malformation in patients with myelomeningocele. Child’s Brain 1975;1:255-259.
dc.relationHaines SJ, Berger M. Current treatment of Chiari malformations types I and II: a survey of the pediatric section of the American Association of Neurological Surgeons. Neurosurgery 1991;28:353-357.
dc.relationRuge JR, Masciopinto J, Storrs BB, McLone DG. Anatomical progression of the Chiari II malformation. Child’s Nerv Syst 1992;8:86-91.
dc.relationVenes JL, Black KL, Latack JT. Preoperative evaluation and surgical management of the Arnold-Chiari II malformation. J Neurosurg 1986;64:363-370.
dc.relationMilerad J, Lagercrantz H, Johnson P. Obstructive sleep apnea in Arnold-Chiari malformation treated with acetazolamide. Acta Paediatr 1992;81:609-612.
dc.relationMorley AR. Laryngeal stridor, Arnold Chiari malformation and medullary haemorrhages. Dev Med Child Neurol 1969;11:471-474.
dc.relationGozal D, Arens R, Omlin KJ, Jacobs RA, Keens TG. Peripheral chemoreceptor function in children with myelomeningocele and Arnold-Chiari malformation type 2. Chest 1995;108:425-431.
dc.relationMori K Nishimura T. Electrophysiological studies on brainstem function in patients with myelomeningocele. Pediatr Neurosurg 1995;22:120-131.
dc.relationWorley G, Erwin CW, Schuster JM, et al. Baeps in infants with myelomeningocele and later development of Chiari II malformation-related brainstem dysfunction. Dev Med Child Neurol 1994;36:707-715.
dc.rightsopen access
dc.subjectMielomeningocele
dc.subjectMalformação de Chiari do Tipo II
dc.subjectMalformação de Arnold-Chiari
dc.subjectDesconpressão de Fossa Craniana Posterior
dc.subjectHidrocefalia
dc.subjectParalisia de Cordas Vocais
dc.subjectMyelomeningocele
dc.subjectChiari type II Malformation
dc.subjectArnold-Chiari Malformation
dc.subjectPosterior Fossa Decompression
dc.subjectHydrocephalus
dc.subjectVocal Cord Paralysis
dc.titleMalformação de chiari do tipo II sintomática
dc.typeArticle


Este ítem pertenece a la siguiente institución