Calcifying epithelial odontogenic tumor (CEOT) or Pindborg tumor is a rare, benign neoplasm of odontogenic origin, which accounts for about 0.4% to 3% of all odontogenic tumors. This lesion was described as a distinct entity for the first time by Pindborg in 1955 and was designated as Pindborg tumor in 1967. Intraosseous location of the tumor is the most common, accounting for about 94% of the cases reported thus far, but an extraosseous or peripheral variant was also described by Pindborg in 1966 and corresponds to approximately 6% of all cases of CEOT.