Desmoplastic small round cell tumor of the kidney mimicking wilms tumor: A case report and review of the literature

dc.contributorPathology Laboratory,Imperatriz
dc.contributorPathology Reference Laboratory
dc.contributorUniversidade Estadual Paulista (Unesp)
dc.contributorUniversidade de São Paulo (USP)
dc.date.accessioned2014-05-27T11:24:03Z
dc.date.accessioned2022-10-05T18:18:25Z
dc.date.available2014-05-27T11:24:03Z
dc.date.available2022-10-05T18:18:25Z
dc.date.created2014-05-27T11:24:03Z
dc.date.issued2009-12-01
dc.identifierApplied Immunohistochemistry and Molecular Morphology, v. 17, n. 6, p. 557-562, 2009.
dc.identifier1541-2016
dc.identifier1533-4058
dc.identifierhttp://hdl.handle.net/11449/71281
dc.identifier10.1097/PAI.0b013e3181a3b8b8
dc.identifierWOS:000272362100015
dc.identifier2-s2.0-74249105607
dc.identifier.urihttp://repositorioslatinoamericanos.uchile.cl/handle/2250/3920480
dc.description.abstractDesmoplastic small round cell tumor (DSRCT) is a rare, aggressive, malignant neoplasm usually present with the widespread abdominal serosal involvement and affects mainly adolescents and young adults. When presenting within visceral organs, as kidney, the diagnosis of DSRCT imposes significant difficulties. We present a case of primary DSRCT of the kidney in a 10-year-old boy mimicking clinically and pathologically Wilms tumor. The tumor showed morphologic and immunohistochemical features of DSRCT and the presence of the Ewing sarcoma and Wilm tumor 1 fusion transcripts resulting from the t(11;22) (p13;q12) reciprocal translocation. DSRCT should be considered in the differential diagnosis of Wilm tumor and other small blue-round cell tumors of the kidney. © 2009 by Lippincott Williams & Wilkins.
dc.languageeng
dc.relationApplied Immunohistochemistry and Molecular Morphology
dc.relation2.042
dc.relation0,765
dc.relation0,765
dc.rightsAcesso restrito
dc.sourceScopus
dc.subjectDesmoplastic small round cell tumor
dc.subjectKidney
dc.subjectSmall round cell tumor
dc.subjectWilms tumor
dc.subjectRNA binding protein EWS
dc.subjectWT1 protein
dc.subjectbone metastasis
dc.subjectcancer chemotherapy
dc.subjectcancer morphology
dc.subjectcancer radiotherapy
dc.subjectcancer staging
dc.subjectcase report
dc.subjectchild
dc.subjectcomputer assisted tomography
dc.subjectdesmoplastic small round cell tumor
dc.subjectdifferential diagnosis
dc.subjectfusion gene
dc.subjecthuman
dc.subjecthuman tissue
dc.subjectimmunohistochemistry
dc.subjectkidney
dc.subjectlung metastasis
dc.subjectmale
dc.subjectnephrectomy
dc.subjectnephroblastoma
dc.subjectpriority journal
dc.subjectradiation dose
dc.subjectreciprocal chromosome translocation
dc.subjectschool child
dc.subjectthorax radiography
dc.subjectCarcinoma, Small Cell
dc.subjectChild
dc.subjectChromosomes, Human, Pair 11
dc.subjectChromosomes, Human, Pair 22
dc.subjectDiagnosis, Differential
dc.subjectHumans
dc.subjectImmunohistochemistry
dc.subjectKidney Neoplasms
dc.subjectMale
dc.subjectOncogene Proteins, Fusion
dc.subjectTumor Markers, Biological
dc.subjectWilms Tumor
dc.titleDesmoplastic small round cell tumor of the kidney mimicking wilms tumor: A case report and review of the literature
dc.typeArtigo


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