Artículos de revistas
Microangiopathy of the inner ear, deafness, and cochlear implantation in a patient with Susac syndrome
Fecha
2011Registro en:
ACTA OTO-LARYNGOLOGICA, v.131, n.10, p.1123-1128, 2011
0001-6489
10.3109/00016489.2011.593549
Autor
BITTENCOURT, Aline Gomes
SANTOS, Andrea Felice Dos
GOFFI-GOMEZ, Maria Valeria Schmidt
KUTSCHER, Kellen
TSUJI, Robinson Koji
BRITO, Rubens De
BENTO, Ricardo Ferreira
Institución
Resumen
Conclusion: The cochlear implant was beneficial as an attempt to restore hearing and improve communication abilities in this patient with profound sensorineural hearing loss secondary to Susac syndrome. Objective: To report the audiological outcomes of cochlear implantation (CI) in a young woman with Susac syndrome after a 6-month follow-up period. Susac syndrome is a rare disorder. It is clinically characterized by a typical triad of sensorineural deafness, encephalopathy, and visual defect, due to microangiopathy involving the brain, inner ear, and retina. Methods: This was a retrospective review of a case at a tertiary referral center. After diagnosis, the patient was evaluated by a multidisciplinary team and received a cochlear implant in her right ear. Results: The patient achieved 100% open-set sentence recognition in noise conditions and 92% monosyllable and 68% medial consonant recognition in quiet conditions after 6 months of implant use. She reported the use of the telephone 3 months after activation.