This case report describes a successful aesthetic and functional reconstruction of a patient who had severe maxilla bony deficiency as a result of excision of central giant cell granuloma. Initially, the lesion was curetted plus peripheral ostectomy. The defect was reconstructed with iliac bone graft in a second step, with both surgeries performed under general anesthesia. Six months after second step, later vertical distraction osteogenesis was performed on the grafted maxilla to obtain a satisfactory bony height. Distraction osteogenesis can be a good alternative for the reconstruction of bone deficiencies associated to bone graft; however, it should be not done as first treatment in the severe pathologic jaw defects.18126-31