dc.creatorRibeiro, Jose Dirceu
dc.creatorRibeiro, Maria Angela G de O
dc.creatorRibeiro, Antonio Fernando
dc.date
dc.date2015-11-27T12:49:30Z
dc.date2015-11-27T12:49:30Z
dc.date.accessioned2018-03-29T00:56:58Z
dc.date.available2018-03-29T00:56:58Z
dc.identifierJornal De Pediatria. v. 78 Suppl 2, p. S171-86
dc.identifier0021-7557
dc.identifier
dc.identifierhttp://www.ncbi.nlm.nih.gov/pubmed/14676856
dc.identifierhttp://repositorio.unicamp.br/jspui/handle/REPOSIP/195262
dc.identifier14676856
dc.identifier.urihttp://repositorioslatinoamericanos.uchile.cl/handle/2250/1295495
dc.descriptionCystic fibrosis has become, in the last 70 years, the most important potentially fatal inherited disease that affects white individuals around the world. Although it is considered a genetic disorder, which strikes cells of different organs, not all patients present similar clinical response. Many clinical manifestations, mainly pulmonary and gastrointestinal, may develop in cystic fibrosis patients. The aim of this article is to offer pediatricians an updated review of the controversies and recent advances in the treatment of cystic fibrosis. Systematic review in the Medline database. Seventy-nine articles about cystic fibrosis published in international journals were reviewed. This article presents an updated and critical review of the main events related to the incidence, pathophysiology, diagnosis and treatment of cystic fibrosis. Even though no treatment is available for this disease, new findings about its etiology and pathophysiology have been discovered in the last two decades, improving treatment and survival of cystic fibrosis patients.
dc.description78 Suppl 2
dc.descriptionS171-86
dc.languagepor
dc.relationJornal De Pediatria
dc.relationJ Pediatr (Rio J)
dc.rightsaberto
dc.rights
dc.sourcePubMed
dc.title[controversies In Cystic Fibrosis--from Pediatrician To Specialist].
dc.typeArtículos de revistas


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