Caroli's Disease: 6 Case Studies

dc.creatorAlves De Tommaso A.M.
dc.creatorMoreira Santos D.S.
dc.creatorHessel G.
dc.date2003
dc.date2015-06-30T17:28:51Z
dc.date2015-11-26T15:41:08Z
dc.date2015-06-30T17:28:51Z
dc.date2015-11-26T15:41:08Z
dc.date.accessioned2018-03-28T22:49:36Z
dc.date.available2018-03-28T22:49:36Z
dc.identifier
dc.identifierActa Gastroenterologica Latinoamericana. , v. 33, n. 1, p. 47 - 51, 2003.
dc.identifier3009033
dc.identifier
dc.identifierhttp://www.scopus.com/inward/record.url?eid=2-s2.0-25144482825&partnerID=40&md5=557f513e2392d6dc1059621c24a22ffe
dc.identifierhttp://www.repositorio.unicamp.br/handle/REPOSIP/102200
dc.identifierhttp://repositorio.unicamp.br/jspui/handle/REPOSIP/102200
dc.identifier2-s2.0-25144482825
dc.identifier.urihttp://repositorioslatinoamericanos.uchile.cl/handle/2250/1264541
dc.descriptionCaroli's disease is characterized by congenital non-obstructive dilatation of the intrahepatic bile ducts of undefined etiology. It is a rare disease usually affecting the whole liver but it may affect a lobe or a segment (11). This study shows the evolution of 6 cases (2 boys and 4 girls) that were diagnosed with Caroli's disease at a referral service. Their ages ranged from 2 to 16 years - median age 10 years. One of the patients presented with cholangitis, while hepatomegaly was observed in 83% of the cases. Four of the patients presented biliary lithiasis and in one of these cholesterol crystals could be observed in the duodenal secretion. The diagnosis was confirmed in 4 cases by endoscopic retrograde cholangiopancreatography, in 1 by cholangioresonance and 1 by echography. Two of the patients also presented congenital hepatic fibrosis. The outpatient clinic follow-up indicated that all the patients evolved well with the exception of one patient who was selected as a candidate for liver transplantation.
dc.description33
dc.description1
dc.description47
dc.description51
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dc.languageen
dc.publisher
dc.relationActa Gastroenterologica Latinoamericana
dc.rightsaberto
dc.sourceScopus
dc.titleCaroli's Disease: 6 Case Studies
dc.typeArtículos de revistas


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