Linear chronic discoid lupus erythematosus is a rare manifestation of cutaneous lupus in which erythematous, atrophic, dyschromic lesions are located along the lines of Blaschko. This report describes the case of a 15-year old boy with a 2-year history of discoid, erythematous, hyper and hypopigmented lesions with central atrophy, situated along the lines of Blaschko on his right arm. Histopathology showed epidermal atrophy, hyperkeratosis, follicular plugging, thickening of the basement membrane zone, and superficial and deep chronic perivascular and periadnexal inflammatory infiltrate, with dermal mucin deposit, thus confirming diagnosis. A total of 14 cases have been described of this variant, the onset of which is often in childhood. There is no difference in incidence between genders. Lesions most commonly develop on the face. There have been no reports of any association with systemic disease. © 2011 by Anais Brasileiros de Dermatologia.863553556Daldon, P.E.C., (2003) Lúpus Eritematoso Hipertrófico: Estudo Clínico-patológico De 14 Pacientes, , [Tese]. Campinas (SP): Universidade Estadual de CampinasRockmann, H., Feller, G., Schadendorf, D., Goerdt, S., Subacute cutaneous lupus erythematosus on the lines of blaschko (2006) Eur J Dermatol, 16, pp. 302-306Julià, M., Mascaró Jr., J.M., Guilabert, A., Navarra, E., Ferrando, J., Herrero, C., Sclerodermiform linear lupus erythematosus: A distinct entity or coexistence of two autoimmune diseases? (2008) J Am Acad Dermatol, 58, pp. 665-667Lee, M.W., Choi, J.H., Sung, K.J., Moon, K.C., Koh, J.K., Linear cutaneous lupus erythematosus in the lines of blaschko (2001) Pediatr Dermatol, 18, pp. 396-399Seitz, C.S., Brocker, E.B., Trautmann, A., Linear variant of chronic cutaneous lupus erythematosus: A clue for the pathogenesis of chronic cutaneous lupus erythematosus? (2008) Lupus, 17, p. 1136Gaitanis, G., Nomikos, K., Chaniotakis, I., Stergiopoulou, C., Zioga, A., Bassukas, I., Linear cutaneous lupus erythematosus: A subset of childhood cutaneous lupus erythematosus (2009) Lupus, 18, pp. 759-761Abe, M., Ishikawa, O., Myiachi, Y., Linear cutaneous lupus erythematosus following the lines of blaschko (1998) Br J Dermatol, 139, pp. 307-310Nagai, Y., Ishikawa, O., Hattori, T., Ogawa, T., Linear lupus erythematosus profundus on the scalp following the lines of blaschko (2003) Eur J Dermatol, 13, pp. 294-296Requena, C., Torrelo, A., de Prada, I., Zambrano, A., Linear childhood cutaneous lupus erthematosus following blaschko lines (2002) J Eur Acad Dermatol Venereol, 16, pp. 618-620Davies, M.G., Newman, P., Linear cutaneous lupus erythematosus in association with ipsilateral submandibular myoepithelial sialadenitis (2001) Clin Exp Dermatol, 26, pp. 56-58Abe, M., Ohnishi, K., Ishikawa, O., Guess what? Linear cutaneous lupus erythematous (LCLE): Relationship with Blaschko's lines (2000) Eur J Dermatol, 10, pp. 229-231Green, J.J., Baker, D.J., Linear childhood discoid lupus erythematosus following the lines of blaschko: A case report with review of the linear manifestations of lupus erythematosus (1999) Pediatr Dermatol, 16, pp. 128-133Romiti, R., Maragno, L., Arnone, M., Takahashi, M.D.F., Psoríase na infância e adolescência (2009) An Bras Dermatol, 84, pp. 9-22Shapiro, M., Sosis, A.C., Junkins-Hopkins, J.M., Werth, V.P., Lupus erythematosus induced by medications, ultraviolet radiation, and other exogenous agents: A review, with special focus on the development of subacute cutaneous lupus erythematosus in a genetically predisposed individual (2004) Int J Dermatol, 43, pp. 87-94Martin, D.A., Elkon, K.B., Apoptosis (2007) Dubois' Lupus Erythematosus, pp. 118-132. , wallace dj, hayn bh, editors, Philadelphia: Lippincott Willians & Willians