Multiple Desmoid Tumors In A Patient With Gardner's Syndrome - Report Of A Case

dc.creatorPinheiro L.V.
dc.creatorFagundes J.J.
dc.creatorCoy C.S.R.
dc.creatorCabello C.
dc.creatorToro I.
dc.creatorMichellino M.
dc.creatorFachina P.H.
dc.creatorWard M.
dc.creatorLeal R.F.
dc.creatorAyrizono M.D.L.S.
dc.date2014
dc.date2015-06-25T17:55:58Z
dc.date2015-11-26T14:41:52Z
dc.date2015-06-25T17:55:58Z
dc.date2015-11-26T14:41:52Z
dc.date.accessioned2018-03-28T21:49:07Z
dc.date.available2018-03-28T21:49:07Z
dc.identifier
dc.identifierInternational Journal Of Surgery Case Reports. Elsevier Ltd, v. 5, n. 7, p. 370 - 374, 2014.
dc.identifier22102612
dc.identifier10.1016/j.ijscr.2014.04.018
dc.identifierhttp://www.scopus.com/inward/record.url?eid=2-s2.0-84901330787&partnerID=40&md5=7fa21658e954d24c65ee95c8664caac2
dc.identifierhttp://www.repositorio.unicamp.br/handle/REPOSIP/86928
dc.identifierhttp://repositorio.unicamp.br/jspui/handle/REPOSIP/86928
dc.identifier2-s2.0-84901330787
dc.identifier.urihttp://repositorioslatinoamericanos.uchile.cl/handle/2250/1251039
dc.descriptionINTRODUCTION Desmoid tumor (DT) is a common manifestation of Gardner's Syndrome (GS), although it is a rare condition in the general population. DT in patients with GS is usually located in the abdominal wall and/or intra-abdominal cavity. PRESENTATION OF CASE We report a case of a 32 years-old female patient with familial adenomatous polyposis (FAP), who was already submitted to total colectomy and developed multiple DT, located in the abdominal wall and in the left breast. The patient underwent several surgical procedures, with a multidisciplinary team of surgeons. Wide surgical resections of the left breast and the abdominal wall tumors were performed in separate steps. Polypropylene mesh reconstruction and muscle flaps were needed to cover the defects of the thoracic and abdominal walls. After partial necrosis of the adipose-cutaneous flap in the abdomen that required a new skin graft, she had a satisfactory outcome with complete healing of the surgical incisions. DISCUSSION DT is frequent in GS, however, breast localization is very rare, with few cases reported in the literature. Recurrence of DT is not negligible, even after a wide surgical resection. GS patients must be followed up closely, and clinical examination, associated with imaging studies, should be performed to detect any signs of tumor. CONCLUSION DT represents one of the most significant causes of the morbidity and mortality that affects FAP patients following colectomy. In general, the surgical procedures to excise DT are highly complex, requiring a multidisciplinary team. © 2014 The Authors.
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dc.languageen
dc.publisherElsevier Ltd
dc.relationInternational Journal of Surgery Case Reports
dc.rightsaberto
dc.sourceScopus
dc.titleMultiple Desmoid Tumors In A Patient With Gardner's Syndrome - Report Of A Case
dc.typeArtículos de revistas


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