Clinical Manifestations And Oral Findings In Fraser Syndrome

dc.creatorDiniz M.B.
dc.creatorLima L.M.
dc.creatorSacono N.T.
dc.creatorDe Paula A.B.
dc.creatorDos Santos-Pinto L.
dc.date2007
dc.date2015-06-30T18:51:53Z
dc.date2015-11-26T14:38:57Z
dc.date2015-06-30T18:51:53Z
dc.date2015-11-26T14:38:57Z
dc.date.accessioned2018-03-28T21:44:20Z
dc.date.available2018-03-28T21:44:20Z
dc.identifier
dc.identifierJournal Of Dentistry For Children. , v. 74, n. 3, p. 231 - 235, 2007.
dc.identifier15518949
dc.identifier
dc.identifierhttp://www.scopus.com/inward/record.url?eid=2-s2.0-47949113498&partnerID=40&md5=8bc390a524eede012d1f39f64ef73022
dc.identifierhttp://www.repositorio.unicamp.br/handle/REPOSIP/105135
dc.identifierhttp://repositorio.unicamp.br/jspui/handle/REPOSIP/105135
dc.identifier2-s2.0-47949113498
dc.identifier.urihttp://repositorioslatinoamericanos.uchile.cl/handle/2250/1249802
dc.descriptionThis article is the first known case report of Fraser syndrome in the dental literature. Its purpose was to present the clinical manifestations, oral findings, and dental treatment of a 14-year, 10-month-old female patient. Fraser syndrome is a rare recessive autosomal genetic disorder characterized by multisystemic malformation, usually comprising cryptophthalmos, syndactyly, and renal defects. The child presented with: (1) hydrocephaly; (2) face asymmetry; (3) low-inserted ears; (4) flat nose bridge; (5) cryptophthalmos; (6) bilateral absence of eyeballs; (7) hypertelorism; (8) syndactyly on the left fingers and toes; (9) skeletal defects; and (10) lower limb asymmetry. The intraoral examination revealed: (1) complete primary denture; (2) malocclusion; (3) tooth crowding; (4) ogival palate; (5) normal labial frena; (6) absence of lingual frenum (not compromising the tongue movements); (7) parched lips; (8) supragingival calculus adhered to all tooth surfaces; and (9) moderate gingivitis. The dental treatment consisted of periodic monitoring of the patient's oral health status and supragingival scaling associated with topical applications of 0.12% chlorhexidine digluconate gel at 2-week intervals to reduce gingivitis.
dc.description74
dc.description3
dc.description231
dc.description235
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dc.languageen
dc.publisher
dc.relationJournal of Dentistry for Children
dc.rightsfechado
dc.sourceScopus
dc.titleClinical Manifestations And Oral Findings In Fraser Syndrome
dc.typeArtículos de revistas


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