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Mostrando ítems 11-20 de 32
O papel da amônia sobre as alterações comportamentais, neuroinflamação e apoptose em um modelo experimental de acidemia metilmalônica.
(Universidade Federal de Santa MariaBrasilFarmacologiaUFSMPrograma de Pós-Graduação em FarmacologiaCentro de Ciências da Saúde, 2017-08-29)
Methylmalonic acidemia is an autosomal recessive metabolism biochemically characterized by
a deficiency in the activity of the mutase methylmalonyl-CoA and the tissue accumulation of
methylmalonate (MMA). In this acidemia, ...
Mitochondrial permeability transition in neuronal damage promoted by Ca2+ and respiratory chain complex II inhibition
(Blackwell Publishing LtdOxfordInglaterra, 2004)
Prostaglandina E2 potencializa as convulsões induzidas por metilmalonato
(Universidade Federal de Santa MariaBRFarmacologiaUFSMPrograma de Pós-Graduação em Farmacologia, 2009-11-23)
Methylmalonic acidemias comprehend a group of innate error of the metabolism (EIM)characterized clinically and biochemically for the tissue accumulation of acid methylmalonic (MMA)and neurological dysfunction, including ...
Neurotoxidade Neonatal do Metilmalonato é suficiente para iniciar déficit de memória em camundongos: envolvimento de marcadores inflamatórios e apoptóticos
(Universidade Federal de Santa MariaBRFarmacologiaUFSMPrograma de Pós-Graduação em Farmacologia, 2014-06-28)
The methylmalonic acidemia is an inborn error of metabolism (IEM) characterized by methylmalonic acid (MMA) accumulation in body fluids and tissues, causing neurological dysfunction, mitochondrial failure, oxidative stress ...
Acidemia propiónica neonatal con deterioro neurológico, rechazo al alimento y emesis reporte de caso y revisión de la literatura
(Sociedad de Cirugía de Bogotá, Hospital de San José y Fundación Universitaria de Ciencias de la Salud, 2012-12-01)
Atividade anticonvulsivante do óleo de peixe
(Universidade Federal de Santa MariaBRFarmacologiaUFSMPrograma de Pós-Graduação em Farmacologia, 2010-08-18)
Methylmalonic acidemias are inherited metabolic disorders characterized by methylmalonate (MMA) accumulation and neurological dysfunction, including seizures. Dietary fatty acids are known as an important energy source and ...