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Do not forget to check the scalp in systemic light-chain amyloidosis
(2021)
Systemic light chain amyloidosis (AL) is a nonproliferative plasma cell disorder in which fragments of immunoglobulin deposit in tissues. Clinical manifestations are often nonspecific, making diagnosis challenging.Biopsy ...
Cardiac amyloidosis secondary to waldenström macroglobulinemia
(Editorial Ciencias Medicas, 2020-01-01)
Introduction: Waldenström's macroglobulinemia is a hematological neoplasm belonging to the group of monoclonal gammopathies, which includes systemic symptoms and those related to an increase in M paraprotein. Objective: ...
Head and neck amyloidosis: clinicopathological features and immunohistochemical analysis of 14 cases
(Wiley-blackwellMaldenEUA, 2012)
A Single Mutation at the Sheet Switch Region Results in Conformational Changes Favoring lambda 6 Light-Chain Fibrillogenesis
(ACADEMIC PRESS LTD- ELSEVIER SCIENCE LTD, 2010)
Systemic amyloid light-chain (LC) amyloidosis is a disease process characterized by the pathological deposition of monoclonal LCs in tissue. All LC subtypes are capable of fibril formation although lambda chains, particularly ...
Guía de Práctica Clínica para el diagnóstico de la amiloidosis: Parte 1/3. Año 2020Clinical practice guidelines for diagnosis of amyloidosis: Part 1/3. Year 2020Guia de prática clínica para o diagnóstico e tipificação da amiloidose: Parte 1/3. Ano 2020
(Universidad Nacional de Córdoba. Facultad de Ciencias Médicas, 2021-03-12)
Métodos: Se generó un listado de preguntas con el formato PICO centradas en la especificidad y sensibilidad de las pruebas diagnósticas en amiloidosis. Se realizó la búsqueda en PubMed durante julio-agosto del 2019, en ...
Monoclonal gammopathy of renal significance (MGRS): real-world data on outcomes and prognostic factors
(Wiley, 2022)
Monoclonal gammopathy of renal significance (MGRS) is a recognized clinical entity. Literature regarding treatment and its outcomes in MGRS is sparse due to the rarity and misdiagnosis of MGRS. We retrospectively analyzed ...
Usos del Angulo de fase en algunas enfermedades crónico degenerativas
La bioimpedancia eléctrica está siendo cada vez más reconocida gracias al uso de nuevas prácticas clínicas para evaluar el estado de pacientes con enfermedades crónico degenerativas, permitiendo que a través de las variables ...