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Rare diagnosis of Ebstein anomaly in an adult patient in Northern Rio de Janeiro
(HCPA/FAMED/UFRGS, 2021)
Ebstein anomaly associated with cri du chat (cat's cry) syndrome and 20q duplication
Ebstein anomaly is a congenital heart defect with a low prevalence and high mortality in the early stages of life. In medical literature, there is no reported association between Ebstein anomaly and cri du chat syndrome. ...
A técnica do cone para correção da anomalia de Ebstein: resultados imediatos e em longo prazo
(Sociedade Brasileira de Cardiologia - SBC, 2011)
FUNDAMENTO: As principais correções da anomalia de Ebstein (AE) baseiam-se na reconstrução monocúspide da valva tricúspide e são limitadas pela frequente necessidade de substituição ou pela alta reincidência de insuficiência ...
Displasia congénita de la válvula tricúspide (anomalía de ebstein). A propósito de un caso en varón de 40 años.
(Ciencia Digital Editorial, 2018)
Ebstein anomaly associated with cri du chat (cat’s cry) syndrome and 20q duplication
Ebstein anomaly is a congenital heart defect with a low prevalence and high mortality in the early stages of life. In medical literature, there is no reported association between Ebstein anomaly and cri du chat syndrome. ...
Caso clínico: adulto con anomalía de Ebstein
(2020)
Introduction: Ebstein's anomaly is characterized by low implantation of the septal and posterior tricuspid leaflets; therefore, the right atrium is wide and its ventricle is small. Being a rather rare pathology ...
La aplicabilidad de la ecocardiografía tridimensional como mejor método diagnóstico en la anomalía de Ebstein en la población infantil (0 a 17 años) del Hospital del Niño Francisco de Icaza Bustamante desde enero del 2011 a diciembre del 2014
(Universidad de Guayaquil. Facultad de Ciencias Médicas. Carrera de Medicina, 2015)
La anomalía de Ebstein es una enfermedad rara. Su diagnóstico y manejo terapéutico precoz modifica los índices de morbilidad y mortalidad. Investigamos como la ecocardiografía tridimensional es una herramienta diagnostica. ...
Identification of clinically relevant phenotypes in patients with Ebstein anomaly
(2018)
Background: Ebstein anomaly (EA) is a heterogeneous congenital heart defect (CHD), frequently accompanied by diverse cardiac and extracardiac comorbidities, resulting in a wide range of clinical outcomes. Hypothesis: ...