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Altered Prion Protein Expression Pattern in CSF as a Biomarker for Creutzfeldt-Jakob Disease
(PUBLIC LIBRARY SCIENCE, 2012)
Altered prion protein expression pattern in csf as a biomarker for creutzfeldt-jakob disease
(PUBLIC LIBRARY SCIENCE, 2012)
MM1+2C Sporadic Creutzfeldt-Jakob Disease Presenting as Rapidly Progressive Nonfluent Aphasia
(IOS Press, 2014-01)
We report a 77-year-old man, presenting with progressive aphasia as an initial symptom, who developed severe dementia over the course of 20 months. Frontal cortex PrPSc western blot was type 2 and codon 129 was MM; brain ...
MM2 subtype of sporadic Creutzfeldt-Jakob disease may underlie the clinical presentation of progressive supranuclear palsy
(Springer HeidelbergHeidelbergAlemanha, 2013)
Clinical and electrophysiological evolution of a case of sporadic creutzfeldt-jakob disease [Evolución clínica y electroencefalográfica de un caso de probable enfermedad de Creutzfeldt-Jakob esporádica]
(2012)
Introduction: Creutzfeldt-Jakob disease is manifested by a rapidly progressive dementia, myoclonus and periodic sharp wave complexes in biphasic or triphasic EEG. It is required for definitive diagnosis a histopathological ...
Epidemiología de la enfermedad de Creutzfeldt Jakob de Chile entre los años 2001 a 2007 : estudio de tasas regionales de morbimortalidad
(Universidad de Chile, 2011)
La Enfermedad de Creutzfeldt–Jakob es la encefalopatía espongiforme humana más común, producida por una proteína infectante llamada prion, el cual es codificado en el gen PRNP del cromosoma 20. Ésta tiene una distribución ...