Buscar
Mostrando ítems 11-20 de 116
Solid-state bioprocessing of sugarcane bagasse with Auricularia fuscosuccinea for phenolic compounds extraction
(Taylor & Francis, 2021-10)
Sugarcane bagasse is a natural source of phenolic compounds. However, these compounds are bound to lignocellulose components, reducing their ability to function as good antioxidants. These linkages are hydrolyzed by enzymes ...
Purificação e caracterização parcial de uma B-D glicosidase de Artemia franciscana com ação sobre celobiose e lactose
(Universidade Federal do Rio Grande do NorteBRUFRNPrograma de Pós-Graduação em BioquímicaBioquímica; Biologia Molecular, 2008-02-27)
-D-glucosidase (EC 3.2.1.21) is one of the most interesting glycosidases, especially for hydrolysis cellobiose releasing glucose, is last step degradation of cellulose. This function makes the -D-glucosidase is of great ...
Enfermedad de Pompe : descripción de las características clínicas y de laboratorio de una familia colombianaPompe disease : clinical presentation in a colombian family
(Asociación Colombiana de NeurologíaGrupo de Investigación Clínica en Enfermedades del Niño y del Adolescente - PediacienciasBogotá, Colombia, 2021)
Uso de assinaturas estruturais para proposta de mutações em enzimas β-glicosidase usadas na produção de biocombustíveis
(Universidade Federal de Minas GeraisBrasilICB - INSTITUTO DE CIÊNCIAS BIOLOGICASICX - DEPARTAMENTO DE CIÊNCIA DA COMPUTAÇÃOPrograma de Pós-Graduação em BioinformaticaUFMG, 2019-03-11)
β-glucosidases (EC 3.2.1.21) are key enzymes in the second-generation biofuel production. They act synergically with endoglucanases and exoglucanases in the conversion of biomass to fermentable sugars. However, most known ...
Generalized glycogenosis in Brahman-derived breeds: diagnosis and prevalence in Argentina
(Springer, 2019-08)
Generalized glycogenosis is a lethal autosomal recessive disease caused by a deficient activity of the acidic 1,4-α-glucosidase enzyme and characterized by an accumulation of glycogen within lysosomes. Three mutations in ...
Pompe disease in a Brazilian series: clinical and molecular analyses with identification of nine new mutations
(Springer International, 2014)
Relato do primeiro paciente brasileiro com a forma infantil da doença de Pompe tratado com alfa-glicosidase recombinante humana
(Sociedade Brasileira de Pediatria, 2008)
Objetivo: Relatar o primeiro caso de forma infantil da doença de Pompe tratado no Brasil. Descrição: Trata-se de doença de depósito lisossomal que se caracteriza por defeitos da enzima alfa-glicosidase ácida, com acúmulo ...