Artículos de revistas
Controversies In Cystic Fibrosis - From Pediatrician To Specialist [controvérsias Na Fibrose Cística - Do Pediatra Ao Especialista]
Registro en:
Jornal De Pediatria. , v. 78, n. SUPPL. 2, p. S171 - S186, 2002.
217557
2-s2.0-0036866333
Autor
Ribeiro J.D.
Ribeiro M.A.G.D.O.
Ribeiro A.F.
Institución
Resumen
Objective: Cystic fibrosis has become, in the last 70 years, the most important potentially fatal inherited disease that affects white individuals around the world. Although it is considered a genetic disorder, which strikes cells of different organs, not all patients present similar clinical response. Many clinical manifestations, mainly pulmonary and gastrointestinal, may develop in cystic fibrosis patients. The aim of this article is to offer pediatricians an updated review of the controversies and recent advances in the treatment of cystic fibrosis. Sources: systematic review in the Medline database. Summary of the findings: seventy-nine articles about cystic fibrosis published in international journals were reviewed. This article presents an updated and critical review of the main events related to the incidence, pathophysiology, diagnosis and treatment of cystic fibrosis. 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