Artículos de revistas
Maxillofacial Mazabraud’s syndrome: a case report & review
Fecha
2018Registro en:
J Stomatol Oral Maxillofac Surg, 119 (2018): 44–48
Autor
Domancic Alucema, Francisco
Pezoa, N.
Fernández Toro, María de los Ángeles
Ortega Pinto, Ana
Donoso Hofer, Francisca
Institución
Resumen
Mazabraud’s syndrome is characterized by myxomas of intramuscular type present in association with
fibrous dysplasia. Up to this day, approximately 80 cases of Mazabraud’s syndrome have been reported,
although in the head and neck territory intramuscular myxoma reports in association with fibrous
dysplasia of the bone are very scarce. An unusual case of Mazabraud’s syndrome in a 63 years old female
displaying fibrous dysplasia of the mandible and soft tissue myxoma in the edentulous alveolar ridge in the
molar area is reported. After four years of follow-up, the clinical, imagenological and microscopical findings
that led to the diagnosis and treatment are discussed. This report exemplifies the diagnostic and treatment
challenge of this rare disease and enhances our clinical knowledge due to its long follow-up, highlighting
the need of understanding better its behavior in order to establish proper guidelines for its treatment.