Artículos de revistas
Nevoid Basal-cell Syndrome: Literature Review And Case Report In A Family.
Registro en:
São Paulo Medical Journal = Revista Paulista De Medicina. , v. 113, n. 3, p. 917 - 921, 1995.
15163180
2-s2.0-0029296078
Autor
Jose Tincani A.
Santos Martins A.
Gomes Andrade R.
Franco Mello Jr. E.J.
Camargo Bueno M.A.
Institución
Resumen
The Nevoid Basal-Cell Carcinoma Syndrome (NBCC), or as it is also referred to, basal-cell nevus syndrome or Gorlin-Goltz syndrome, is characterized by multiple early-appearing basal cell carcinomas, keratocytosis of the mandible, and anomalies of the ocular, skeletal reproductive system. We describe four patients in the same family, all of them possessing a large number of skin tumors associated with other typical clinical and X-Ray anomalies of NBCC. The definitive treatment of NBCC has yet to be established, however, early diagnosis is very important as well as the periodical follow-up examination of ten patients, mainly due to the transformations in the skin lesions that may occur. 113 3 917 921