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        Implementation of chromosomal microarrays in a cohort of patients with intellectual disability at the Argentinean public health system 

        Espeche, Lucia Daniela; Solari, Andrea Paula; Mori, María Ángeles; Arenas, Rubén Martín; Palomares, María; Pérez, Myriam; Martínez, Cinthia; Lotersztein, Vanesa; Segovia, Mabel; Armando, Romina; Dain, Liliana Beatriz; Nevado, Julián; Lapunzina, Pablo; Rozental, Sandra (Springer, 2020-09-13)
        Intellectual disability is a neurodevelopmental disorder in which genetic, epigenetic and environmental factors are involved. In consequence, the determination of its etiology is usually complex. Though many countries have ...

        Chromosomal microarray analysis in the genetic evaluation of 279 patients with syndromic obesity 

        D’Angelo, Carla Sustek; Silva, Monica Castro Varela Rodrigues da; Fabris, Cláudia Irene Emilio de Castro; Otto, Paulo Alberto; Perez, Ana Beatriz Alvarez; Lourenço, Charles Marques; Kim, Chong Ae; Bertola, Debora Romeo; Kok, Fernando; Garcia-Alonso, Luis; Koiffmann, Celia Priszkulnik (BioMed Central, 2018)
        Abstract Background Syndromic obesity is an umbrella term used to describe cases where obesity occurs with additional phenotypes. It often arises as part of a distinct ...

        Chromosomal microarray analysis in the genetic evaluation of 279 patients with syndromic obesity 

        D'Angelo, Carla Sustek; Varela, Monica Castro; Emilio de Castro, Claudia Irene; Otto, Paulo Alberto; Alvarez Perez, Ana Beatriz [UNIFESP]; Lourenco, Charles Marques; Kim, Chong Ae; Bertola, Debora Romeo; Kok, Fernando; Garcia-Alonso, Luis [UNIFESP]; Koiffmann, Celia Priszkulnik (Biomed Central Ltd, 2018)
        Background: Syndromic obesity is an umbrella term used to describe cases where obesity occurs with additional phenotypes. It often arises as part of a distinct genetic syndrome with Prader-Willi syndrome being a classical ...

        Investigation of selected genomic deletions and duplications in a cohort of 338 patients presenting with syndromic obesity by multiplex ligation-dependent probe amplification using synthetic probes 

        D'Angelo, Carla Sustek; Varela, Monica C; Fabris, Cláudia Irene Emilio de Castro; Kim, Chong Ae; Bertola, Débora Romeo; Lourenço, Charles M; Perez, Ana Beatriz A; Koiffmann, Celia Priszkulnik (BioMed Central Ltd.London, 2014-10-31)
        Background Certain rare syndromes with developmental delay or intellectual disability caused by genomic copy number variants (CNVs), either deletions or duplications, are associated with higher rates of obesity. Current ...

        Consensus Statement: Chromosomal Microarray Is a First-Tier Clinical Diagnostic Test for Individuals with Developmental Disabilities or Congenital Anomalies 

        MILLER, David T.; ADAM, Margaret P.; ARADHYA, Swaroop; BIESECKER, Leslie G.; BROTHMAN, Arthur R.; CARTER, Nigel P.; CHURCH, Deanna M.; CROLLA, John A.; EICHLER, Evan E.; EPSTEIN, Charles J.; FAUCETT, W. Andrew; FEUK, Lars; FRIEDMAN, Jan M.; HAMOSH, Ada; JACKSON, Laird; KAMINSKY, Erin B.; KOK, Klaas; KRANTZ, Ian D.; KUHN, Robert M.; LEE, Charles; OSTELL, James M.; ROSENBERG, Carla; SCHERER, Stephen W.; SPINNER, Nancy B.; STAVROPOULOS, Dimitri J.; TEPPERBERG, James H.; THORLAND, Erik C.; VERMEESCH, Joris R.; WAGGONER, Darrel J.; WATSON, Michael S.; MARTIN, Christa Lese; LEDBETTER, David H. (CELL PRESS, 2010)
        Chromosomal microarray (CMA) is increasingly utilized for genetic testing of individuals with unexplained developmental delay/intellectual disability (DD/ID), autism spectrum disorders (ASD), or multiple congenital anomalies ...

        Genomic Imbalances In Syndromic Congenital Heart Disease 

        Coelho Molck M.; Simioni M.; Paiva Vieira T.; Sgardioli I.C.; Paoli Monteiro F.; Souza J.; Fett-Conte A.C.; Félix T.M.; Lopes Monlléo I.; Gil-da-Silva-Lopes V.L. (Elsevier Editora Ltda, 2016)

        Investigação citogenômica em pacientes com cardiopatias congênitas 

        Ribeiro-Bicudo, Lucilene Arilho [UNESP]; Moretti-Ferreira, Danilo [UNESP]; Universidade Estadual Paulista (Unesp) (Universidade Estadual Paulista (Unesp), 2018-05-04)
        As cardiopatias congênitas (CCs) podem ser definidas como qualquer anormalidade na estrutura e/ou na função cardiocirculatória presente ao nascimento. Constituem as malformações congênitas mais comuns entre recém-nascidos ...

        Análise cromossômica por microarranjos aplicada à identificação de alterações genômicas em pacientes com fissura lábio palatina 

        Silva, Heglayne Pereira Vital da (BrasilUFRNPROGRAMA DE PÓS-GRADUAÇÃO EM CIÊNCIAS DA SAÚDE, 2019-11-12)
        Non-syndromic orofacial clefts (OFC) consist of craniofacial malformations characterized by the presence of abnormal spaces or gaps in the upper lip, alveolus and/or palate, which may have effects on speech, hearing, ...

        Doenças cardíacas congênitas (DCCS) : investigação de etiologia genética 

        Figueiredo, Ana Carolina Vaqueiro (2022-09-06)
        As doenças cardíacas congênitas (DCCs) são definidas como alterações estruturais no coração e nos grandes vasos presentes ao nascimento. Acometem em todo o mundo de 1 a 5% de todos os nascidos vivos, sendo, portanto, o ...

        Aplicabilidade de redes PPI em Biologia de sistemas no contexto da síndrome de Williams-Beuren 

        Ribeiro-Bicudo, Lucilene Arilho [UNESP]; Gamba, Bruno Faulin; Universidade Estadual Paulista (Unesp) (Universidade Estadual Paulista (Unesp), 2022-02-07)
        Uma microdeleção hemizigótica de 1,5Mb a 1,8Mb na região do braço longo do cromossomo 7 (7q11.23) ocasiona uma doença genética rara multigênica. Faces típicas, doenças cardiovasculares, alterações do tecido conjuntivo ...
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        Red de Repositorios Latinoamericanos
        + of 4.000.000
        Available publications
        163 Participating institutions
        Dirección de Servicios de Información y Bibliotecas (SISIB)
        Universidad de Chile
        Membership Login
        Featured collections
        • Latin American Theses
        • Argentinean Theses
        • Chilean Theses
        • Peruvian Theses
        Latest collections added
        • Argentina
        • Brazil
        • Colombia
        • México
        Dirección de Servicios de Información y Bibliotecas (SISIB)
        Universidad de Chile
        Red de Repositorios Latinoamericanos | 2006-2018