Artículos de revistas
Camurati-engelmann Disease: Failure Of Response To Bisphosphonates: Report Of Two Cases.
Registro en:
Clinical Rheumatology. v. 24, n. 4, p. 398-401, 2005-Aug.
0770-3198
10.1007/s10067-004-1056-7
15660289
Autor
Castro, Glaucio R W
Appenzeller, Simone
Marques-Neto, João Francisco
Bértolo, Manoel B
Samara, Adil M
Coimbra, Ibsen
Institución
Resumen
Camurati-Engelmann disease is a rare bone disorder characterized by cortical thickening of the diaphysis of tubular bones, with sparing of the epiphysis. It has variable degrees of penetrance and expression, but may be very disabling for the affected individuals who manifest the painful symptoms. The authors report on two women with typical presentation of severe Camurati-Engelmann disease whose treatment with bisphosphonates failed to add any improvement beyond that elicited by corticosteroids alone. 24 398-401